JOINT COMMITTEE ON INFANT HEARINGJoint Committee on Infant Hearing 2007 Summary
Following are the principles of the Joint Committee on Infant Hearing (JCIH) 2007 Position Statement:
RISK INDICATORS ASSOCIATED WITH PERMANENT CONGENITAL, DELAYED-ONSET OR PROGRESSIVE HEARING LOSS IN CHILDHOOD
(Joint Committee on Infant Hearing Position Statement, 2007)
The timing and number of hearing reevaluations for children with risk factors should be customized and individualized depending on the relative likelihood of a subsequent delayed-onset hearing loss.
Infants who pass the neonatal screening but have any of the other risk factor should have at least 1 diagnostic audiology assessment by 24 to 30 months of age.
RISK INDICATORS ASSOCIATED WITH PERMANENT CONGENITAL, DELAYED-ONSET, OR PROGRESSIVE HEARING LOSS IN CHILDHOOD
Risk indicators that are marked with a "§" are of greater concern for delayed-onset hearing loss:
1. Caregiver concern§ regarding hearing, speech, language, or developmental delay.
2. Family history§ of permanent childhood hearing loss.
3. Neonatal intensive care of more than 5 days or any of the following regardless of length of stay: ECMO,§
assisted ventilation, exposure to ototoxic medications (gentimycin and tobramycin) or loop diuretics (furosemide/Lasix), and hyperbilirubinemia that requires exchange transfusion.
4. In utero infections, such as CMV,§ herpes, rubella, syphilis, and toxoplasmosis.
5. Craniofacial anomalies, including those that involve the pinna, ear canal, ear tags, ear pits, and temporal bone anomalies.
6. Physical ﬁndings, such as white forelock, that are associated with a syndrome known to include a sensorineural or permanent conductive hearing loss.
7. Syndromes associated with hearing loss or progressive or late-onset hearing loss,§ such as neuroﬁbromatosis, osteopetrosis, and Usher syndrome131; other frequently identiﬁed syndromes include Waardenburg, Alport, Pendred, and Jervell and LangeNielson.
8. Neurodegenerative disorders,§ such as Hunter syndrome, or sensory motor neuropathies, such as Friedreich ataxia and Charcot-Marie-Tooth syndrome.
9. Culture-positive postnatal infections associated with sensorineural hearing loss,§ including conﬁrmed bacterial and viral (especially herpes viruses and varicella) meningitis.
10. Head trauma, especially basal skull/temporal bone fracture§ that requires hospitalization.
PEDIATRICS Volume 120, Number 4, October 2007